Association of von Recklinghausen's neurofibromatosis with adult polycystic disease of kidneys and liver.

نویسندگان

  • S C Varma
  • K K Talwar
  • S P Kaushik
  • B K Sharma
چکیده

Introduction Von Recklinghausen's neurofibromatosis and adult polycystic disease of the kidneys (APDK) are both heredofamilial disorders (Preiser and Davenport, 1918; Dalgaard, 1971) although sporadic cases also occur (Wander and Dsgupta, 1977; Hatfield and Pfister, 1972). Both the conditions are known to occur in association with a number of other hereditary disorders (Dalgaard, 1971; Koch, 1977). However, their occurrence together is a rarity (Siegelman, Javed and Hecht, 1971).

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عنوان ژورنال:
  • Postgraduate medical journal

دوره 58 676  شماره 

صفحات  -

تاریخ انتشار 1982